Pulmonary extranodal marginal zone lymphoma of mucosa-associated lymphoid tissue associated with granulomatous inflammation in a child with chromosome 22q11.2 deletion syndrome (digeorge syndrome)

Tawatchai PongpruttipanJames R. CookMiguel Reyes-MugicaJonathan E. SpahrSteven H. SwerdlowUniversity of Pittsburgh School of MedicineMahidol UniversityCleveland Clinic FoundationUniversity of Pittsburgh Medical Center, Children's Hospital of Pittsburgh2018-06-112018-06-112012-11-01Journal of Pediatrics. Vol.161, No.5 (2012)10976833002234762-s2.0-84867864228https://repository.li.mahidol.ac.th/handle/20.500.14594/14577Patients with immunodeficiency disorders have an increased incidence of lymphoproliferative disorders; however, only 4 such patients with DiGeorge/chromosome 22q11.2 deletion syndrome have been reported. We report a case of a pulmonary Epstein-Barr virus-negative extranodal marginal zone lymphoma of mucosa-associated lymphoid tissue in a child with this syndrome. Copyright © 2012 Mosby Inc.Mahidol UniversityMedicinePulmonary extranodal marginal zone lymphoma of mucosa-associated lymphoid tissue associated with granulomatous inflammation in a child with chromosome 22q11.2 deletion syndrome (digeorge syndrome)ArticleSCOPUS10.1016/j.jpeds.2012.07.003