Phadungsak SangsoadPatkawat RamartPornpim KorpraphongVilasinee RerkpichaisuthKanapon PradniwatJitsupa TreetipsatitFaculty of Medicine, Siriraj Hospital, Mahidol University2020-01-272020-01-272019-05-01Urology Case Reports. Vol.24, (2019)221444202-s2.0-85067211821https://repository.li.mahidol.ac.th/handle/123456789/51663© 2019 Immunoglobulin G4-related disease is a systemic disease, recognized as extensive T-lymphocyte and IgG4-positive plasma cells. It can present as inflammatory pseudotumor in various organs. A female 75 years old, diagnosed IgG4-related autoimmune pancreatitis, presented with urinary retention. Pelvic examination showed well-defined, soft tissue mass, bulging from anterior vaginal wall. MRI pelvis demonstrated a huge periurethral mass, size 6.2 × 4.4 × 4.2 cm, encasing the urethra, extending from bladder neck to distal urethra, and mimicking the prostate gland. Tissue biopsy showed compatible with IgG4-related disease. Immunosuppresive drugs were given for few months and the patient could void normally.Mahidol UniversityMedicineArticleSCOPUS10.1016/j.eucr.2019.100844