Publication: Successful treatment of a child with Schwartz-Jampel syndrome using rapid maxillary expansion and CPAP
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Issued Date
2021-03-01
Resource Type
ISSN
15509397
15509389
15509389
Other identifier(s)
2-s2.0-85102537434
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Mahidol University
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SCOPUS
Bibliographic Citation
Journal of Clinical Sleep Medicine. Vol.17, No.3 (2021), 601-604
Suggested Citation
Supakit Peanchitlertkajorn, Thanate Assawakawintip, Mevadee Pibulniyom, Panida Srisan, Patimaporn Pungchanchaikul, Rasintra Jaroenying Successful treatment of a child with Schwartz-Jampel syndrome using rapid maxillary expansion and CPAP. Journal of Clinical Sleep Medicine. Vol.17, No.3 (2021), 601-604. doi:10.5664/jcsm.9028 Retrieved from: https://repository.li.mahidol.ac.th/handle/123456789/78385
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Title
Successful treatment of a child with Schwartz-Jampel syndrome using rapid maxillary expansion and CPAP
Abstract
Study Objectives:We reported an 8-year-old male patient with Schwartz-Jampel syndrome, severe obstructive sleep apnea, constricted maxilla and moderate tonsillar hypertrophy. The syndrome is characterized by myotonia, skeletal dysplasia, and facial dysmorphism. Methods: CPAP was initially prescribed, but he was not able to tolerate due to a high pressure setting. Rapid maxillary expansion alone reduced AHI to 10.4 events/h. Results: When combined with CPAP, AHI is further reduced to 2.4 events/h. The patient has a better compliance with CPAP following rapid maxillary expansion therapy as the pressure setting decreased. Conclusions: This is the first report utilizing a combination of rapid maxillary expansion and CPAP therapy to successfully treat severe pediatric OSA.