Publication: Polycythemia vera concomitant with renal angiomyolipoma: Case report and clinical outcome
Issued Date
2017-02-01
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ISSN
1875855X
19057415
19057415
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2-s2.0-85015987817
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Mahidol University
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SCOPUS
Bibliographic Citation
Asian Biomedicine. Vol.11, No.1 (2017), 89-92
Suggested Citation
Supat Chamnanchanunt, Pravinwan Thungthong, Niphon Praditphol, Kunapa Iam-Arunthai, Jirapong Dowreang, Chajchawan Nakhakes, Tawatchai Suwanban Polycythemia vera concomitant with renal angiomyolipoma: Case report and clinical outcome. Asian Biomedicine. Vol.11, No.1 (2017), 89-92. doi:10.5372/1905-7415.1101.543 Retrieved from: https://repository.li.mahidol.ac.th/handle/20.500.14594/41985
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Title
Polycythemia vera concomitant with renal angiomyolipoma: Case report and clinical outcome
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Abstract
Background: Polycythemia vera has been found in a wide range of hematopoietic tissue disorders, but rarely concomitant with renal abnormality. To our knowledge there is only one available report of a patient with polycythemia vera concomitant with renal angiomyolipoma, and the report does not cover the clinical course of this rare finding. Objectives: To report the presentation and clinical course of a patient with polycythemia vera concomitant with right renal angiomyolipoma. Methods: We retrospectively reviewed the medical records of a patient with polycythemia vera who presented with renal angiomyolipoma. Results: Our patient presented with a right renal mass and polycythemia vera diagnosed by a point mutation in the gene for Janus kinase 2. The mass was diagnosed as renal angiomyolipoma on histopathology. After partial nephrectomy, she was prescribed a low dosage of hydroxyurea without the return of erythrocytosis for a year. Conclusions: Polycythemia vera responded well to low dosage hydroxyurea, which controlled erythrocytosis after removing the renal mass.