Publication: Fetal long QT syndrome manifested as atrioventricular block and ventricular tachycardia: A case report and a review of the literature
Issued Date
2013-12-01
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ISSN
14321971
01720643
01720643
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2-s2.0-84889569489
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Mahidol University
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SCOPUS
Bibliographic Citation
Pediatric Cardiology. Vol.34, No.8 (2013), 1955-1962
Suggested Citation
Sanitra Anuwutnavin, Prapat Wanitpongpan, Paweena Chungsomprasong, Jarupim Soongswang, Nattinee Srisantiroj, Tuangsit Wataganara Fetal long QT syndrome manifested as atrioventricular block and ventricular tachycardia: A case report and a review of the literature. Pediatric Cardiology. Vol.34, No.8 (2013), 1955-1962. doi:10.1007/s00246-012-0507-1 Retrieved from: https://repository.li.mahidol.ac.th/handle/20.500.14594/32054
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Fetal long QT syndrome manifested as atrioventricular block and ventricular tachycardia: A case report and a review of the literature
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Abstract
Fetal onset of congenital long QT syndrome (LQTS) is a rare manifestation, and prenatal diagnosis is difficult. This report describes a boy who presented with both atrioventricular (AV) block and ventricular tachycardia during the antenatal period. The early postnatal electrocardiogram showed prolongation of the QT interval and AV block, subsequently leading to a polymorphic ventricular tachycardia torsade de pointes. This unique feature of congenital LQTS has a poor outcome, but the boy was successfully treated with beta-blockers and implantation of an automated cardioverter-defibrillator. The intrauterine manifestation of fetal AV block and ventricular tachycardia should raise a high suspicion of congenital LQTS, and the strong association with a malignant clinical course should warrant special evaluation. The literature on the prenatal diagnosis, fetal therapy, and neonatal outcome of this condition also are reviewed. © 2012 Springer Science+Business Media, LLC.