A RARE CASE OF IMMUNOGLOBULIN G4-RELATED DISEASE PRESENTING WITH CORONARY ARTERY PSEUDOTUMOR AND ANEURYSM
Issued Date
2024-01-01
Resource Type
eISSN
22842594
Scopus ID
2-s2.0-85182920641
Journal Title
European Journal of Case Reports in Internal Medicine
Volume
11
Issue
1
Rights Holder(s)
SCOPUS
Bibliographic Citation
European Journal of Case Reports in Internal Medicine Vol.11 No.1 (2024)
Suggested Citation
Koowattanatianchai S., Teawprasert N., Limchareon S., Kaolawanich Y. A RARE CASE OF IMMUNOGLOBULIN G4-RELATED DISEASE PRESENTING WITH CORONARY ARTERY PSEUDOTUMOR AND ANEURYSM. European Journal of Case Reports in Internal Medicine Vol.11 No.1 (2024). doi:10.12890/2023_004215 Retrieved from: https://repository.li.mahidol.ac.th/handle/20.500.14594/95551
Title
A RARE CASE OF IMMUNOGLOBULIN G4-RELATED DISEASE PRESENTING WITH CORONARY ARTERY PSEUDOTUMOR AND ANEURYSM
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Corresponding Author(s)
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Abstract
Immunoglobulin G4-related disease (IgG4-RD) is an autoimmune disease characterized by elevated serum IgG4 levels. It has the potential to affect multiple organs. Despite the diverse manifestations of IgG4-RD, the association with coronary artery disease (CAD) remains poorly understood due to limited evidence. We report the case of a 52-year-old male patient who exhibited typical angina upon exertion, accompanied by elevated serum IgG4 levels. Coronary computed tomographic angiography (CCTA) revealed the presence of pseudotumor formations surrounding and aneurysm changes affecting all coronary arteries, consistent with IgG4-RD. The patient was treated with prednisolone and azathioprine, with the possibility of additional rituximab therapy if symptomatology failed to improve. This case sheds light on the rare occurrence of IgG4-RD with coronary artery involvement and underscores the importance of recognizing this unique clinical entity for appropriate management and further research.