Challenges of managing anomalous mitral arcade with severe mitral regurgitation and hydrops fetalis in infants
Issued Date
2024-06-12
Resource Type
eISSN
1757790X
Scopus ID
2-s2.0-85196102701
Pubmed ID
38866580
Journal Title
BMJ case reports
Volume
17
Issue
6
Rights Holder(s)
SCOPUS
Bibliographic Citation
BMJ case reports Vol.17 No.6 (2024)
Suggested Citation
Trisauvapak T., Bongkotwilawan N., Ekawaravong S. Challenges of managing anomalous mitral arcade with severe mitral regurgitation and hydrops fetalis in infants. BMJ case reports Vol.17 No.6 (2024). doi:10.1136/bcr-2023-259272 Retrieved from: https://repository.li.mahidol.ac.th/handle/123456789/98918
Title
Challenges of managing anomalous mitral arcade with severe mitral regurgitation and hydrops fetalis in infants
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Abstract
Anomalous mitral arcade (MA) is a rare congenital anomaly. We report a case of MA in a newborn who presented with hydrops fetalis due to severe mitral regurgitation. After birth, he developed severe respiratory failure, congestive heart failure and airway obstruction because an enlarged left atrium from severe mitral regurgitation compressed the distal left main bronchus. There is limited experience in surgical management of this condition in Thailand, and the patient's mitral valve was too small for replacement. Therefore, he was treated with medication to control heart failure and supported with positive pressure ventilation to promote growth. We have followed the patient until the current time of writing this report at the age of 2 years, and his outcome is favourable regarding heart failure symptoms, airway obstruction, growth and development. This case describes a challenging experience in the non-surgical management of MA with severe regurgitation, which presented at birth.